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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Hemangioendothelioma: A rare case of a primary intracardiac tumor
Pediatric Cardiology, Volume 34, No. 1, Year 2013
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Description
Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach-Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor. © 2012 Springer Science+Business Media, LLC.
Authors & Co-Authors
Beaton, Andrea Zawacki
United States, Washington, D.c.
Childrens National Health System
Kuttler, Trevor
United States, Bethesda
Walter Reed National Military Medical Center
Hassan, Ali
Kuwait, Safat
Chest Diseases Hospital Kuwait
Nath, Dilip Sri
United States, Washington, D.c.
Childrens National Health System
Reyes, Christine
United States, Washington, D.c.
Childrens National Health System
Jonas, Richard A.
United States, Washington, D.c.
Childrens National Health System
Martin, Gerard Robert
United States, Washington, D.c.
Childrens National Health System
Statistics
Citations: 7
Authors: 7
Affiliations: 3
Identifiers
Doi:
10.1007/s00246-012-0280-1
ISSN:
01720643
e-ISSN:
14321971
Research Areas
Cancer