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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
Global, regional, and national burden of congenital heart disease, 1990–2017: a systematic analysis for the Global Burden of Disease Study 2017
The Lancet Child and Adolescent Health, Volume 4, No. 3, Year 2020
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Description
Background: Previous congenital heart disease estimates came from few data sources, were geographically narrow, and did not evaluate congenital heart disease throughout the life course. Completed as part of the Global Burden of Diseases, Injuries, and Risk Factors Study 2017, this study aimed to provide comprehensive estimates of congenital heart disease mortality, prevalence, and disability by age for 195 countries and territories from 1990 to 2017. Methods: Mortality estimates were generated for aggregate congenital heart disease and non-fatal estimates for five subcategories (single ventricle and single ventricle pathway congenital heart anomalies; severe congenital heart anomalies excluding single ventricle heart defects; critical malformations of great vessels, congenital valvular heart disease, and patent ductus arteriosus; ventricular septal defect and atrial septal defect; and other congenital heart anomalies), for 1990 through to 2017. All available global data were systematically analysed to generate congenital heart disease mortality estimates (using Cause of Death Ensemble modelling) and prevalence estimates (DisMod-MR 2·1). Systematic literature reviews of all types of congenital anomalies to capture information on prevalence, associated mortality, and long-term health outcomes on congenital heart disease informed subsequent disability estimates. Findings: Congenital heart disease caused 261 247 deaths (95% uncertainty interval 216 567–308 159) globally in 2017, a 34·5% decline from 1990, with 180 624 deaths (146 825–214 178) being among infants (aged <1 years). Congenital heart disease mortality rates declined with increasing Socio-demographic Index (SDI); most deaths occurred in countries in the low and low-middle SDI quintiles. The prevalence rates of congenital heart disease at birth changed little temporally or by SDI, resulting in 11 998 283 (10 958 658–13 123 888) people living with congenital heart disease globally, an 18·7% increase from 1990 to 2017, and causing a total of 589 479 (287 200–973 359) years lived with disability. Interpretation: Congenital heart disease is a large, rapidly emerging global problem in child health. Without the ability to substantially alter the prevalence of congenital heart disease, interventions and resources must be used to improve survival and quality of life. Our findings highlight the large global inequities in congenital heart disease and can serve as a starting point for policy changes to improve screening, treatment, and data collection. Funding: Bill & Melinda Gates Foundation. © 2020 The Author(s). Published by Elsevier Ltd. This is an Open Access article under the CC BY 4.0 license
Available Materials
https://efashare.b-cdn.net/share/pmc/articles/PMC7645774/bin/mmc1.pdf
Authors & Co-Authors
Zimmerman, Meghan S.
Unknown Affiliation
Smith, Alison Grace Carswell
Unknown Affiliation
Sable, Craig Andrew
Unknown Affiliation
Echko, Michelle Marie
Unknown Affiliation
Wilner, Lauren B.
Unknown Affiliation
Olsen, Helen Elizabeth
Unknown Affiliation
Atalay, Hagos Tasew
Unknown Affiliation
Bhutta, Zulfiqar A.
Unknown Affiliation
Castro, Franz F.
Unknown Affiliation
Cortesi, Paolo Angelo
Unknown Affiliation
Dubey, Manisha
Unknown Affiliation
Fischer, Florian
Unknown Affiliation
Hamidi, Samer A.
Unknown Affiliation
Hay, Simon I.
Unknown Affiliation
Hoang, Chi Linh
Unknown Affiliation
Hugo-Hamman, Christopher T.
Unknown Affiliation
Jenkins, Kathy J.
Unknown Affiliation
Khalil, Ibrahim A.
Unknown Affiliation
Kumar, R. Krishna
Unknown Affiliation
Kwan, Gene F.
Unknown Affiliation
Mengistu, Desalegn Tadese
Unknown Affiliation
Mokdad, Ali H.I.
Unknown Affiliation
Naghavi, Mohsen
Unknown Affiliation
Negesa, Lemma B.
Unknown Affiliation
Negoi, Ionut
Unknown Affiliation
Negoi, Ruxandra Irina
Unknown Affiliation
Nguyen, Cuong Tat
Unknown Affiliation
Nguyen, Huong Lan Thi
Unknown Affiliation
Nguyen, Son Hoang
Unknown Affiliation
Nguyen, Trang Huyen Thi
Unknown Affiliation
Nixon, Molly R.
Unknown Affiliation
Noubiap, Jean Jacques
Unknown Affiliation
Patel, Shanti N.
Unknown Affiliation
Peprah, Emmanuel Kwame
Unknown Affiliation
Reiner, Robert Charles
Unknown Affiliation
Roth, Gregory A.
Unknown Affiliation
Temsah, Mohamad Hani
Unknown Affiliation
Tovani-Palone, Marcos Roberto
Unknown Affiliation
Towbin, Jeffrey A.
Unknown Affiliation
Tran, Bach Xuan
Unknown Affiliation
Truong, Nu Thi
Unknown Affiliation
Vos, Theo
Unknown Affiliation
Weintraub, Robert G.
Unknown Affiliation
Weldegwergs, Kidu Gidey
Unknown Affiliation
Zaidi, Zoubida
Unknown Affiliation
Zheleva, Bistra
Unknown Affiliation
Zühlke, Liesl Joanna
Unknown Affiliation
Murray, Christopher J.L.
Unknown Affiliation
Martin, Gerard Robert
Unknown Affiliation
Kassebaum, Nicholas J.
Unknown Affiliation
Statistics
Citations: 275
Authors: 50
Identifiers
Doi:
10.1016/S2352-4642(19)30402-X
ISSN:
23524642
Research Areas
Disability
Health System And Policy
Maternal And Child Health
Noncommunicable Diseases
Violence And Injury
Study Design
Cross Sectional Study
Grounded Theory
Study Approach
Systematic review