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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Management of spinal cord compression caused by extramedullary hematopoiesis in beta-thalassemia
Internal Medicine, Volume 47, No. 12, Year 2008
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Description
Thalassemia is a chronic hemolytic anemia, endemic around the Mediterranean basin. Extramedullary hematopoiesis (EMH) is a normal compensatory reaction that can involve many organs or tissues, including the epidural space, leading to a spinal cord compression syndrome. In almost all cases, the clinical and MR patterns are those of a lower dorsal spinal cord progressive compression secondary to an epidural expanding process. The management still remains controversial, including mainly blood transfusions, decompressive surgery and radiotherapy. We present a case of EMH in a thalassemic adolescent boy presenting with a T12 level of compression, treated successfully with blood transfusion, surgical decompression and radiotherapy. © 2008 The Japanese Society of Internal Medicine.
Authors & Co-Authors
Berhouma, Moncef
France, Lyon
Hopital Neurologique et Neurochirurgical Pierre Wertheimer
Hafedh, Jemel
Tunisia, Tunis
Institut National de Neurologie Mongi-ben Hamida
Statistics
Citations: 28
Authors: 2
Affiliations: 2
Identifiers
Doi:
10.2169/internalmedicine.47.0890
ISSN:
09182918
e-ISSN:
13497235
Research Areas
Cancer
Health System And Policy
Participants Gender
Male