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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
immunology and microbiology
Nailfold capillaroscopy characteristics of antisynthetase syndrome and possible clinical associations: Results of a multicenter international study
Journal of Rheumatology, Volume 46, No. 3, Year 2019
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Description
Objective. To describe nailfold videocapillaroscopy (NVC) features of patients with antisynthetase syndrome (AS) and to investigate possible correlations with clinical and serological features of the disease. Methods. We retrospectively analyzed NVC images of 190 patients with AS [females/males 3.63, mean age 49.7 ± 12.8 yrs, median disease duration 53.7 mos (interquartile range 82), 133 anti-Jo1 and 57 non-anti-Jo1-positive patients]. For each patient, we examined number of capillaries, giant capillaries, microhemorrhages, avascular areas, ramified capillaries, and the presence of systemic sclerosis (SSc)-like pattern. Finally, we correlated NVC features with clinical and serological findings of patients with AS. Concomitantly, a historical cohort of 75 patients with antinuclear antibody-negative primary Raynaud phenomenon (RP) and longterm followup was used as a control group (female/male ratio 4.13/1, mean age 53.9 ± 17.6 yrs) for NVC measures. Results. NVC abnormalities were observed in 62.1% of AS patients compared with 29.3% of primary RP group (p < 0.001). An SSc-like pattern was detected in 67 patients (35.3%) and it was associated with anti-Jo1 antibodies (p = 0.002) and also with a longer disease duration (p = 0.004). Interestingly, there was no significant correlation between the presence of SSc-like pattern and RP, and only 47% of patients with SSc-like pattern had RP. Conclusion. NVC abnormalities are commonly observed in AS, independently from the occurrence of RP. The presence of an SSc-like pattern could allow identification of a more defined AS subtype, and prospective studies could confirm the association with clinical and serological features of AS. © 2019 Journal of Rheumatology. All rights reserved.
Authors & Co-Authors
Sebastiani, Marco
Italy, Modena
Università Degli Studi Di Modena e Reggio Emilia
Manfredi, Andreina
Italy, Modena
Università Degli Studi Di Modena e Reggio Emilia
González-Gay, Miguel Ángel
Unknown Affiliation
Palmou, Natalia
Unknown Affiliation
Cassone, Giulia
Spain, Santander
Universidad de Cantabria
Rojas-Serrano, Jorge
Germany, Frankfurt am Main
Universitätsklinikum Frankfurt
Nuño, Laura
Mexico, Tlalpan
Instituto Nacional de Enfermedades Respiratorias
Giannini, Margherita
Spain, Madrid
Hospital Universitario la Paz
Iannone, Florenzo
Italy, Bari
Università Degli Studi Di Bari Aldo Moro
Vicente-Rabaneda, Esther Francisca
Italy, Bari
Università Degli Studi Di Bari Aldo Moro
Castañeda, Santos
Spain, Madrid
Instituto de Investigación Sanitaria Hospital Universitario de la Princesa
Selva-O'Callaghan, Albert
Spain, Madrid
Instituto de Investigación Sanitaria Hospital Universitario de la Princesa
Emmi, Giacomo
Spain, Barcelona
Hospital Clinic Barcelona
Parisi, Simone
Unknown Affiliation
Cavagna, L.
Unknown Affiliation
Codullo, Veronica
Italy, Pavia
Fondazione Irccs Policlinico San Matteo
Montecucco, Carlomaurizio
Italy, Pavia
Fondazione Irccs Policlinico San Matteo
López-Longo, Francisco Javier
Italy, Pavia
Fondazione Irccs Policlinico San Matteo
Martínez-Barrio, Julia
Spain, Madrid
Hospital General Universitario Gregorio Marañón
Confalonieri, Marco
Italy, Trieste
Azienda Sanitaria Universitaria Giuliano Isontina
Tomietto, Paola
Italy, Trieste
Ospedale Di Cattinara
Sulli, Alberto
Unknown Affiliation
Furini, Federica
Italy, Genoa
Irccs San Martino Polyclinic Hospital
Scirè, Carlo Alberto
Germany, Duisburg
Universität Duisburg-essen
Bortoluzzi, Alessandra
Italy, Ferrara
University of Ferrara
Mosca, Marta
Italy, Pisa
Università Di Pisa
Smith, Vanessa
Germany, Mainz
Universitätsmedizin Mainz
Cutolo, Maurizio
Belgium, Ghent
Universiteit Gent
Statistics
Citations: 39
Authors: 28
Affiliations: 19
Identifiers
Doi:
10.3899/jrheum.180355
ISSN:
0315162X
Research Areas
Health System And Policy
Study Design
Randomised Control Trial
Cohort Study
Participants Gender
Male
Female