Congenital long-QT syndrome in a Nigerian child: a case report.

We describe the clinical manifestation and the challenges of diagnosing Long QT syndrome, type 1 (LQTS1), in an 8-year old girl who presented at the Paediatric Cardiology Clinic with syncopal attacks following dancing and excitement. Her initial ECG showed normal QT interval of 380msec (QTc=440 msec), but later, increased to 410 msec (QTc=520 msec) following epinephrine challenge test. The challenges with the diagnosis of LQTS1 in children in resource-constrained setting and the need for vigilance in children with syncopal attacks and other cardiac events with normal QT intervals on an electrocardiogram are thus highlighted.