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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Nerve Conduction Studies and Electromyography in Friedreich's Ataxia
Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques, Volume 3, No. 4, Year 1976
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Description
Twenty-six of 50 patients were investigated with nerve conduction studies and electromyography using a standard protocol and were compared to the findings in 50 normal control subjects. Almost all cases of typical Friedreich's ataxia had absent sensory action potentials (SAP) in the digital (92%) or sural (96%) nerves. The others had markedly decreased S.A.P's. In these same patients motor conduction auvelocities were either normal or only slightly decreased. In the second, atypical group of 9 patients, the motor conduction velocities were considerably decreased. Because of the absence of sensory action potentials in Friedreich's ataxia, and that the absence was noted in our very mild cases, it is proposed that this measure be used to facilitate early diagnosis. © 1976, Canadian Neurological Sciences Federation. All rights reserved.
Authors & Co-Authors
Bouchard, Jean Pierre
Canada, Montreal
Institut de Recherches Cliniques de Montréal
Lemieux, Bernard G.
Canada, Montreal
Institut de Recherches Cliniques de Montréal
Barbeau, Andrã©
Canada, Montreal
Institut de Recherches Cliniques de Montréal
Statistics
Citations: 42
Authors: 3
Affiliations: 1
Identifiers
Doi:
10.1017/S0317167100025518
ISSN:
03171671