Skip to content
Home
About Us
Resources
Profiles Metrics
Authors Directory
Institutions Directory
Top Authors
Top Institutions
Top Sponsors
AI Digest
Contact Us
Menu
Home
About Us
Resources
Profiles Metrics
Authors Directory
Institutions Directory
Top Authors
Top Institutions
Top Sponsors
AI Digest
Contact Us
Home
About Us
Resources
Profiles Metrics
Authors Directory
Institutions Directory
Top Authors
Top Institutions
Top Sponsors
AI Digest
Contact Us
Menu
Home
About Us
Resources
Profiles Metrics
Authors Directory
Institutions Directory
Top Authors
Top Institutions
Top Sponsors
AI Digest
Contact Us
Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Successful management of bilateral refractory chylothorax after double lung transplantation for lymphangioleiomyomatosis
Annals of Thoracic Medicine, Volume 9, No. 2, Year 2014
Notification
URL copied to clipboard!
Description
Lymphangioleiomyomatosis (LAM) is a rare disease that leads to airways and lymphatic channels obstruction due to abnormal smooth muscle proliferation. It presents with dyspnea, pneumothorax or chylothorax. Lung transplantation (LT) has emerged as a valuable therapeutic option with limited reports. We report a case of LAM that underwent double LT and complicated by refractory bilateral chylothorax which was managed successfully by povidone-iodine pleurodesis and the addition of sirolimus to the post-transplantation immunosuppressive therapy. The patient has no recurrence with 24 months follow-up. Copyright © 2014 by The Saudi Thoracic Society.
Authors & Co-Authors
Hussein, Mohamed
Saudi Arabia, Riyadh
King Faisal Specialist Hospital and Research Centre
Egypt, Cairo
Ain Shams University
Aljehani, Yasser Maher
Saudi Arabia, Riyadh
King Faisal Specialist Hospital and Research Centre
Nizami, Imran Yaqoob
Saudi Arabia, Riyadh
King Faisal Specialist Hospital and Research Centre
Saleh, Waleed Neamatallah
Saudi Arabia, Riyadh
King Faisal Specialist Hospital and Research Centre
Statistics
Citations: 11
Authors: 4
Affiliations: 2
Identifiers
Doi:
10.4103/1817-1737.128862
ISSN:
18171737
e-ISSN:
19983557
Research Areas
Health System And Policy
Study Design
Cohort Study