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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
Mirror hand deformity: A new phenotype with literature review
Revue de Chirurgie Orthopedique et Reparatrice de l'Appareil Moteur, Volume 94, No. 2, Year 2008
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Description
We report the case of a child who presented polydactyly with eight triphalangeal fingers, no thumb or radius and ulnar dimelia. Hand, wrist, forearm and elbow function was compromised, particularly due to wrist stiffness in flexion, the absence of forearm pronation supination and severe limitation of elbow motion. In addition, the child underwent surgery for pyloric hypertrophy and also presented a multicystic kidney. We present the clinical, anatomic, electromyographic, genetic and therapeutic aspects of this rare deformity and discuss data presented in the literature. © 2007 Elsevier Masson SAS. All rights reserved.
Authors & Co-Authors
El Hage, S.
Lebanon, Beirut
Hôtel-dieu de France Hospital
Ghanem, Ismat B.
Lebanon, Beirut
Hôtel-dieu de France Hospital
Megarbane, Andre
Lebanon, Beirut
Hôtel-dieu de France Hospital
Razzouk, C.
Lebanon, Beirut
Hôtel-dieu de France Hospital
Dagher, Fernand M.
Lebanon, Beirut
Hôtel-dieu de France Hospital
Kharrat, Khalil E.
Lebanon, Beirut
Hôtel-dieu de France Hospital
Statistics
Citations: 7
Authors: 6
Affiliations: 1
Identifiers
Doi:
10.1016/j.rco.2007.09.003
Research Areas
Genetics And Genomics
Health System And Policy
Maternal And Child Health
Study Approach
Systematic review