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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Death in Unverricht - Lundborg disease
Neurological Sciences, Volume 30, No. 4, Year 2009
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Description
The objective of this study is to report cases of unexpected deaths in Unverricht-Lundborg disease (ULD) patients, a comparatively benign form of progressive myoclonus epilepsy. We performed a multicentric study of the circumstances of death in ULD patients seen in the last 16 years. We assessed age, sex, severity and duration of disease, antiepileptic drugs, circumstances and presumed cause of death. Nineteen observations (12 females, 7 males) were collected from four centers (Tunis, Marseille, Milan, Belgrade). The most common causes of death are (1) SUDEP (six cases, all female), with 4/6 on phenobarbital alone, and (2) complications of severe ULD (six cases). Two patients committed suicide. Only one death was clearly unrelated to ULD (car accident), while four patients died of stroke, drowning, complications of chronic alcoholism and Wernicke encephalopathy, respectively. In conclusion, although the prognosis of ULD has progressed, there are still spontaneously severe forms and high risk of early death, including SUDEP. © Springer-Verlag 2009.
Authors & Co-Authors
Khiari, Héla Mrabet
Tunisia, Tunis
Université de Tunis el Manar, Hôpital Charles Nicolle
France, Marseille
Centre Saint-paul Hôpital Henri Gastaut
Franceschetti, Silvana
Italy, Milan
Foundation Irccs Neurological Institute C. Besta
Jovic, Nebojsa
Serbia, Belgrade
Clinic of Neurology and Psychiatry for Children and Youth
Mrabet, Amel
Tunisia, Tunis
Université de Tunis el Manar, Hôpital Charles Nicolle
Genton, Pierre
France, Marseille
Centre Saint-paul Hôpital Henri Gastaut
Statistics
Citations: 14
Authors: 5
Affiliations: 4
Identifiers
Doi:
10.1007/s10072-009-0102-2
ISSN:
15901874
Research Areas
Cancer
Mental Health
Noncommunicable Diseases
Substance Abuse
Participants Gender
Female