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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Mayer-rokitansky-küster-hauser syndrome associated with a urogenital sinus anomaly in a 4-year-old child: Report of a case
Current Urology, Volume 3, No. 2, Year 2009
Notification
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Description
The Mayer-Rokitansky-Küster-Hauser syndrome is a rare entity characterized by congenital aplasia of the vagina and uterus in the presence of normal ovarian function, in conjunction with a 46 XX karyotype. This condition is mostly signalled by primary amenorrhoea around the time of puberty. We report on its diagnosis in a 4-year-old child presenting with urinary incontinence. Also of interest in our index patient is the presence of a pure urogenital sinus anomaly. This extremely rare association has not been previously diagnosed in childhood. © 2009 S. Karger AG, Basel.
Authors & Co-Authors
Adam, Ahmed
Unknown Affiliation
Ebrahim, Zaeem I.
South Africa, Pretoria
University of Pretoria
Engelbrecht, Matthys J.
Unknown Affiliation
Van Heerdena, Izak J.
Unknown Affiliation
Moshokoa, Evelyn M.
Unknown Affiliation
Statistics
Citations: 5
Authors: 5
Affiliations: 1
Identifiers
Doi:
10.1159/000189693
ISSN:
16617649
e-ISSN:
16617657
Research Areas
Health System And Policy
Maternal And Child Health