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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Bilateral renal artery stenosis and epidermal nevus syndrome in a child
Pediatric Nephrology, Volume 26, No. 11, Year 2011
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Description
Epidermal nevus syndrome is a rare congenital sporadic neuro-ectodermic disorder, characterized by the presence of epidermal nevi in association with various developmental abnormalities of the skin, eyes, nervous, skeletal, cardiovascular and urogenital systems. We describe a 5-year-old boy with conjunctival lipodermoid, cervical and facial sebaceous nevi who presented at 3 years of age with hypertension due to bilateral renal artery stenosis together with multiple vascular anomalies (aorta, celiac trunk, superior mesenteric artery) as shown by magnetic resonance angiography. Systemic arterial hypertension was difficult to control despite combined anti-hypertensive drugs and the surgical repair of the aortic coarctation. © 2011 The Author(s).
Authors & Co-Authors
Alsohim, Fahad
France, Lyon
Chu de Lyon
Saudi Arabia, Riyadh
King Saud University
Abou-Jaoude, Pauline
France, Lyon
Chu de Lyon
Ninet, Jean
France, Lyon
Hopital Louis Pradel
Pracros, Jean Pierre
France, Lyon
Chu de Lyon
Phan, Alice
France, Lyon
Chu de Lyon
Cochat, Pierre
France, Lyon
Université de Lyon
Statistics
Citations: 7
Authors: 6
Affiliations: 4
Identifiers
Doi:
10.1007/s00467-011-1949-z
ISSN:
0931041X
e-ISSN:
1432198X
Research Areas
Health System And Policy
Maternal And Child Health
Noncommunicable Diseases
Participants Gender
Male