Hereditary angioedema – How is this managed in preparation for pregnancy?

Introduction and classification of hereditary idiopathic angioedema Hereditary angioedema (HAE) is a rare disease that is inherited in an autosomal dominant fashion. The hallmark of the disease is the development of spontaneous and recurrent episodes of angioedema. Importantly, these episodes of angioedema occur in isolation, without urticaria or pruritis. The disease has no gender predominance. Left untreated, the mortality can be as high as 30 per cent.