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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Proliferative sickle cell retinopathy revealing Glanzmann thrombasthenia
Journal Francais d'Ophtalmologie, Volume 32, No. 10, Year 2009
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Description
Glanzmann thrombasthenia is a rare qualitative platelet abnormality of autosomal recessive transmission caused by absence of GP IIb/IIIa and resulting in disturbance of platelet aggregation and bleeding time extension. We report the case of a 16-year-old female suffering from SC sickle cell disease and presenting with bilateral vitreous hemorrhage revealing Glanzmann thrombasthenia. Despite vitrectomy, the functional prognosis was poor. Indeed, association of a severe hemorrhagic disease and sickle cell retinopathy makes surgical management difficult. © 2009 Elsevier Masson SAS. All rights reserved.
Authors & Co-Authors
Odoulami-Yehouessi, L.
Benin, Cotonou
Centre National Hospitalier et Universitaire
Sounouvou, Ignace
Benin, Cotonou
Centre National Hospitalier et Universitaire
Anani, Ludovic Y.
Benin
Centre National Hospitalier et Universitaire Hubert Koutoukou Maga
Tachabi, S.
Benin, Cotonou
Centre National Hospitalier et Universitaire
Doutentien, C.
Benin, Cotonou
Centre National Hospitalier et Universitaire
Latoundji, Sèmiou B.I.
Benin
Centre National Hospitalier et Universitaire Hubert Koutoukou Maga
Statistics
Citations: 6
Authors: 6
Affiliations: 2
Identifiers
Doi:
10.1016/j.jfo.2009.10.012
ISSN:
01815512
Research Areas
Health System And Policy
Study Approach
Qualitative
Participants Gender
Female