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Publication Details
AFRICAN RESEARCH NEXUS
SHINING A SPOTLIGHT ON AFRICAN RESEARCH
medicine
Nodular lesions of self-healing juvenile cutaneous mucinosis: A Pitfall!
American Journal of Dermatopathology, Volume 34, No. 7, Year 2012
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Description
Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare disorder of unknown origin, which occurs in children in good health. It is characterized by the multiplication of transient cutaneous papules and nodules, mainly located on the head and periarticular areas that spontaneously resolve. Histological features of SHJCM have been well described; therefore, the diagnosis is usually made easily when papules are biopsied. We report a series of 3 new cases of SHJCM presenting mainly with nodular lesions. Histological examination of these nodules showed either lesions consistent with nodular or proliferative fasciitis or nonspecific panniculitis. Mucinous deposits were present but often inconspicuous, so could be disregarded. We wanted to emphasize this misleading presentation because a biopsy for histological examination is always mandatory in cases of proliferating nodules to rule out malignant tumors. Therefore, the diagnosis always requires discussion between pathologists and clinicians to rapidly reassure the parents and avoid inappropriate therapy. Copyright © 2012 by Lippincott Williams & Wilkins.
Authors & Co-Authors
Barreau, Morgane
France, Caen
Université de Caen Normandie
Dompmartin-Blanchère, Anne
France, Caen
Université de Caen Normandie
Jamous, Roula
Lebanon, Beirut
Université Libanaise
Chababi, Myrna
Lebanon, Beirut
Université Libanaise
Soutou, Boutros
Lebanon, Zghorta
Centre Hospitalier du Nord, Lebanon
Reynier-Rezzi, Judith
France, Marseille
Hôpital Saint Joseph
Laplaud, Anne Laure
France, Caen
Université de Caen Normandie
Acher, Aurélie
France, Caen
Chu de Caen Normandie
Rod, Julien
France, Caen
Chu de Caen Normandie
Jeanne-Pasquier, Corinne
France, Caen
Chu de Caen Normandie
Fraïtag, Sylvie R.
France, Paris
Hôpital Necker Enfants Malades
Statistics
Citations: 15
Authors: 11
Affiliations: 6
Identifiers
Doi:
10.1097/DAD.0b013e3182459345
ISSN:
01931091
e-ISSN:
15330311
Research Areas
Cancer
Maternal And Child Health